- Ages Eligible for Study
- 4 years and up
- Genders Eligible for Study
Cystic Fibrosis, Pancreatic Insufficiency, and Bronchiectasis
- National Institute of Diabetes and Digestive and Kidney Diseases (NIDDK)
Patients and family members with known or suspected CF and related disorders of the
respiratory tract or pancreas as defined by clinical presentation, sweat testing and/or
Willingness of patients, or guardian to give informed consent.
Age less than 4 years.
Concomitant medical, psychiatric or other problems which might complicate interpretation of
studies of CF, or for which we are unable to provide adequate care.
Cystic fibrosis is a disease that affects many parts of the body, particularly the lungs and pancreas. The main purpose of this study is to further understand the natural history, clinical presentation, and genetics of cystic fibrosis. Patients with cystic fibrosis will be asked to participate in this study by undergoing standard medical tests and procedures. Patients will have a history taken and have a physical examination as well as blood tests, and a sweat test (a test for cystic fibrosis of the pancreas in which electrolytes are measured in collected sweat). Patients may also be asked to provide samples of urine, stool, and sputum for additional tests. More complicated procedures such as bronchoscopy or bronchoalveolar lavage may be required for diagnosis, treatment, or research purposes. Patients will receive appropriate treatment with antibiotics, pancreatic enzymes, vitamins, physiotherapy, and other agents. Medications may be given by mouth or injected into a vein. This study will provide patients with information on the prognosis of the disease as well as recommendations for management of cystic fibrosis. In addition this study will provide information to researchers which may be useful in other studies of cystic fibrosis.
Contacts and Locations
Please refer to this study by its ClinicalTrials.gov identifier: NCT00001223
National Institutes of Health Clinical Center, 9000 Rockville Pike
Bethesda, Maryland United States
Status: RecruitingContact info For more information at the NIH Clinical Center contact Office of Patient Recruitment (OPR)800-411-1222xTTY8664111010prpl@cc.nih.gov